ARAF protein kinase activates RAS by antagonizing its binding to RASGAP NF1

Mol Cell. 2022 Jul 7;82(13):2443-2457.e7. doi: 10.1016/j.molcel.2022.04.034. Epub 2022 May 24.

Abstract

RAF protein kinases are effectors of the GTP-bound form of small guanosine triphosphatase RAS and function by phosphorylating MEK. We showed here that the expression of ARAF activated RAS in a kinase-independent manner. Binding of ARAF to RAS displaced the GTPase-activating protein NF1 and antagonized NF1-mediated inhibition of RAS. This reduced ERK-dependent inhibition of RAS and increased RAS-GTP. By this mechanism, ARAF regulated the duration and consequences of RTK-induced RAS activation and supported the RAS output of RTK-dependent tumor cells. In human lung cancers with EGFR mutation, amplification of ARAF was associated with acquired resistance to EGFR inhibitors, which was overcome by combining EGFR inhibitors with an inhibitor of the protein tyrosine phosphatase SHP2 to enhance inhibition of nucleotide exchange and RAS activation.

Keywords: ARAF; ERK signaling; NF1; RAS-GTP; drug sensitivity; receptor tyrosine kinase inhibitor.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • ErbB Receptors / genetics
  • ErbB Receptors / metabolism
  • Guanosine Triphosphate / metabolism
  • Humans
  • Neurofibromin 1* / metabolism
  • Protein Binding
  • Proto-Oncogene Proteins A-raf* / metabolism
  • Signal Transduction
  • ras GTPase-Activating Proteins* / metabolism

Substances

  • NF1 protein, human
  • Neurofibromin 1
  • ras GTPase-Activating Proteins
  • Guanosine Triphosphate
  • ErbB Receptors
  • Proto-Oncogene Proteins A-raf