ELX/TEZ/IVA use in cystic fibrosis liver disease: Is the perspective of improved lung function worth the risk?

J Cyst Fibros. 2022 Sep;21(5):881-884. doi: 10.1016/j.jcf.2022.06.008. Epub 2022 Jun 25.
No abstract available

Keywords: CFTR modulator; Cystic fibrosis; Liver transplant; Lung transplant.

Publication types

  • Case Reports

MeSH terms

  • Aminophenols
  • Benzodioxoles
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / epidemiology
  • Cystic Fibrosis* / therapy
  • Humans
  • Liver Diseases* / diagnosis
  • Liver Diseases* / etiology
  • Lung
  • Mutation

Substances

  • Aminophenols
  • Benzodioxoles
  • Cystic Fibrosis Transmembrane Conductance Regulator