Pityriasis rubra pilaris (PRP) is a rare inflammatory skin disease that occurs with phenotypic variability in adults of all ages as well as in children. Data on the treatment of PRP is limited. Here, we report a 5-year-old girl with widespread skin involvement and prominent palmoplantar hyperkeratosis who was initially treated for psoriasis. After reevaluation, a diagnosis of PRP was made, and the patient had an excellent therapeutic response to ustekinumab and acitretin.
Keywords: children; pityriasis rubra pilaris; retinoids; successful treatment; ustekinumab.
© 2022 The Authors. Pediatric Dermatology published by Wiley Periodicals LLC.