Zinner Syndrome with Papillary Neoplasm: A Rare Case Report

J Indian Assoc Pediatr Surg. 2022 Jul-Aug;27(4):473-475. doi: 10.4103/jiaps.jiaps_84_21. Epub 2022 Jul 26.

Abstract

One of the uncommon urogenital malformations in males, which presents late in the second or third decades of life, is the congenital malformation of the seminal vesicle. Zinner syndrome is a rare condition comprising a triad of unilateral renal agenesis, ipsilateral seminal vesicle obstruction, and ipsilateral ejaculatory duct obstruction. Very few cases in the literature describe the malignant change in seminal vesicle cyst in Zinner syndrome. To the best of our knowledge, this is the first report of a papillary neoplasm of the seminal vesicle cyst developed in a patient with Zinner syndrome.

Keywords: Papillary neoplasm in Zinner syndrome; Zinner syndrome; seminal vesicle cyst with malignant transformation; unilateral renal agenesis.

Publication types

  • Case Reports