Improved Kasai Hepatoportoenterostomy Outcomes After Implementation of a Dedicated Biliary Atresia Team

Am Surg. 2023 Dec;89(12):6270-6272. doi: 10.1177/00031348221135781. Epub 2022 Oct 20.

Abstract

It can be difficult or impractical to refer all biliary atresia (BA) patients to high-volume centers. Our hypothesis was that a low volume center could improve outcomes with implementation of a dedicated multidisciplinary BA team. We conducted a retrospective study of patients with BA who underwent hepatic portoenterostomy at our institution from 2003 to 2020, before and after the development of a dedicated BA team. Ten consecutive patients with BA were identified following the establishment of a dedicated BA team. Since the establishment of the BA team, total bilirubin (TB) clearance (TB < 2 mg/dL) achieved by 3 and 6 months has been 60% and 60%, respectively, and survival of the native liver (SNL) at 1 and 2 years post HPE at 90% and 86%, respectively. Outcomes were markedly improved after the team was established. A dedicated BA team prioritizing communication and expeditious workup can improve outcomes at a low volume center.

Keywords: biliary; hepatobiliary; pediatric surgery.

MeSH terms

  • Biliary Atresia* / surgery
  • Bilirubin
  • Humans
  • Liver / surgery
  • Portoenterostomy, Hepatic
  • Retrospective Studies
  • Treatment Outcome

Substances

  • Bilirubin