Background: Immunoglobulin G4-related disease is a rare systemic inflammatory disease that can lead to vascular manifestations such as periarteritis.
Case presentation: A 41-year-old man with stress angina was referred for coronary bypass surgery due to triple vessel coronary disease.
Conclusions: Operative findings revealed significant adhesions and dense peri-coronary and periaortic thickening, also involving the left internal mammary artery. The IgG4-associated disease was confirmed by aortic pathology. The stress angina subsequently improved with the initiation of treatment with prednisone and rituximab.
Keywords: IgG4-related disease; coronary artery disease; coronary vasculitis.
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