Desmoid fibromatosis (DF) arising from musculoaponeurotic structures rarely affects the head and neck region with the abdomen being the most common site of origin. These are benign tumors with locally infiltrative nature usually presenting as painless swellings that are rapidly growing. The infratemporal fossa DF is an extremely rare location with few clinical reports. This article discusses the management of a 2-year-old child with DF of the infratemporal fossa (ITF) along with literature review.
Keywords: Aggressive fibromatosis; Desmoid tumor; Endoscopic; Infratemporal fossa; Mandibulotomy; Pediatric.
© Association of Otolaryngologists of India 2021.