Case Report of Congenital Kyphoscoliosis with Myotonic Dystrophy Type 1: Perioperative and Anesthetic Considerations

J Pediatr Neurosci. 2021 Oct-Dec;16(4):281-284. doi: 10.4103/jpn.JPN_119_20. Epub 2021 Jul 12.

Abstract

Congenital kyphoscoliosis associated with myotonic dystrophy type 1 (DM 1) is a rare combination and carries challenges of surgical as well as anesthetic intervention. The presence of muscular dystrophy may accelerate progression of scoliosis thus requiring surgical treatment. The objective of this case report was to discuss the perioperative anesthetic and surgical management of such cases.

Keywords: Congenital kyphoscoliosis; malignanthyperthermia; myopathy.

Publication types

  • Case Reports