Diagnostic and surgical management of primary central nervous system angioleiomyoma: A case report and literature review

Front Oncol. 2022 Dec 16:12:1072270. doi: 10.3389/fonc.2022.1072270. eCollection 2022.

Abstract

Angioleiomyoma (ALM) is a benign smooth muscle neoplasm that mainly occurs in lower extremities subcutaneous tissue and generally affects middle-aged adults. This tumor histotype may rarely localize intracranially, although only a few cases have been described in the literature. We report a case of intracranial ALM, whose differential diagnosis has been particularly challenging, and firstly provide a comprehensive radiological and intra-operative evaluation of a such rare entity. This represents also the first report of the use of intraoperative confocal microscopy in ALM and the first documented short-term recurrence. At this regard, a scoping literature review has been conducted with the aim of presenting the major clinical and diagnostic features along with the proposed therapeutic strategies.

Keywords: CNS; angiography; angioleiomyoma; fluorescein; intracranial; intraoperative confocal endomicroscopy; primitive.

Publication types

  • Case Reports