A case report of unilateral cerebral vasculitis in adults: keep in mind Lyme neuroborreliosis

BMC Infect Dis. 2023 May 4;23(1):283. doi: 10.1186/s12879-023-08259-z.

Abstract

Background: Lyme neuroborreliosis (LNB), due to infection of the nervous system by the spirochete Borrelia burgdorferi, occurs in 15% of Lyme disease cases. However, neurovascular involvement is uncommon, especially recurrent stroke related to cerebral vasculitis in the absence of CSF pleocytosis.

Case presentation: We report the case of a 58-year-old man without any medical history who exhibited recurrent strokes in the same vascular territory (left internal carotid). Multiple biological screening, neuroimaging methods, and cardiovascular examinations failed to provide a diagnosis and treatment that could have prevented recurrences. Finally, B. burgdorferi sensu lato serology testing in blood and cerebrospinal fluid enabled diagnosis of LNB, in relation to a cerebral vasculitis. The patient experienced no further stroke after four weeks of doxycycline treatment.

Conclusion: B. burgdorferi central nervous system infection must be considered in case of unexplained recurrent and/or multiple strokes, especially if cerebral vasculitis is suspected or demonstrated on neuroimaging.

Keywords: Case report; Lyme; Neuroborreliosis; Stroke; Vasculitis.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Borrelia burgdorferi*
  • Cerebral Infarction
  • Humans
  • Lyme Neuroborreliosis* / complications
  • Lyme Neuroborreliosis* / diagnosis
  • Lyme Neuroborreliosis* / drug therapy
  • Male
  • Middle Aged
  • Stroke* / etiology
  • Vasculitis, Central Nervous System* / diagnosis
  • Vasculitis, Central Nervous System* / drug therapy