SETD2 variation correlates with tumor mutational burden and MSI along with improved response to immunotherapy

BMC Cancer. 2023 Jul 21;23(1):686. doi: 10.1186/s12885-023-10920-4.

Abstract

Background: SETD2 protects against genomic instability via maintenance of homologous recombination repair (HRR) and mismatch repair (MMR) in neoplastic cells. However, it remains unclear whether SETD2 dysfunction is a complementary or independent factor to microsatellite instability-high (MSI-H) and tumor mutational burden-high (TMB-H) for immunocheckpoint inhibitor (ICI) treatment, and little is known regarding whether this type of dysfunction acts differently in various types of cancer.

Methods: This cohort study used multidimensional genomic data of 6726 sequencing samples from our cooperative and non-public GenePlus institute from April 1 through April 10, 2020. MSIsensor score, HRD score, RNAseq, mutational data, and corresponding clinical data were obtained from the TCGA and MSKCC cohort for seven solid tumor types.

Results: A total of 1021 genes underwent target panel sequencing reveal that SETD2 mutations were associated with a higher TMB. SETD2 deleterious mutation dysfunction affected ICI treatment prognosis independently of TMB-H (p < 0.01) and had a lower death hazard than TMB-H in pancancer patients (0.511 vs 0.757). Significantly higher MSI and lower homologous recombination deficiency were observed in the SETD2 deleterious mutation group. Improved survival rate was found in the MSKCC-IO cohort (P < 0.0001) and was further confirmed in our Chinese cohort.

Conclusion: We found that SETD2 dysfunction affects ICI treatment prognosis independently of TMB-H and has a lower death hazard than TMB-H in pancancer patients. Therefore, SETD2 has the potential to serve as a candidate biomarker for ICI treatment. Additionally, SETD2 should be considered when dMMR is detected by immunohistochemistry.

Keywords: Immune checkpoint inhibitors; Microsatellite instability; SETD2 mutation; Tumor microenvironment; Tumor mutation burden.

MeSH terms

  • Asian People
  • Cohort Studies
  • DNA Mismatch Repair / genetics
  • DNA Repair* / genetics
  • Genomic Instability
  • Humans
  • Immunotherapy
  • Microsatellite Instability*
  • Mutation
  • Pancreatic Neoplasms* / genetics
  • Pancreatic Neoplasms* / mortality
  • Recombinational DNA Repair / genetics

Substances

  • SETD2 protein, human