Granulomatosis with polyangiitis (GPA) is a multisystemic necrotizing vasculitis with a special tropism to the respiratory tract and the kidneys. Although uncommon, GPA may be associated with hypereosinophilia and limited organ involvement. In these cases, American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) classification criteria may be insufficient to establish the diagnosis. We described a limited form of GPA, hypereosinophilia, and predominant skin involvement.
Keywords: autoimmune-associated vasculitis; eosinophilic granulomatosis with polyangiitis; erythroderma; granulomatosis with polyangiitis; hypereosinophilia.
Copyright © 2023, Fernandes et al.