Syndrome of megalencephaly, mega corpus callosum, and complete lack of motor development: an unusual case and a literature review

Childs Nerv Syst. 2024 Jan;40(1):219-225. doi: 10.1007/s00381-023-06150-5. Epub 2023 Sep 9.

Abstract

The syndrome of megalencephaly, mega corpus callosum (MEG-MegaCC) accompanied by complete lack of motor development is a rare condition with only few sporadic cases having been reported in the literature. In this paper, we describe a child from non-consanguineous parents presenting with MegaCC, psychomotor retardation, and language impairment linked to MEG-MegaCC syndrome. Genetic analysis, radiological findings, and detailed neurological phenotype of MEG-MegaCC syndrome with its overlapping syndromes would allow for a better classification of the disease spectrum.

Keywords: Developmental delay; Macrocephaly; Mega corpus callosum; Megalencephaly; Psychomotor retardation.

Publication types

  • Review
  • Case Reports

MeSH terms

  • Agenesis of Corpus Callosum / complications
  • Agenesis of Corpus Callosum / diagnostic imaging
  • Child
  • Corpus Callosum / diagnostic imaging
  • Humans
  • Megalencephaly* / complications
  • Megalencephaly* / diagnostic imaging
  • Nervous System Malformations*
  • Syndrome