Purpose: To present a rare case of diabetic striatopathy in a child with type 1 diabetes mellitus with reversible unilateral hemichorea hemiballismus.
Conclusion: A high index of suspicion is required to make a diagnosis of DS in children presenting with abnormal movement disorder and characteristic neuroimaging findings in a background of uncontrolled DM.
Keywords: Diabetes mellitus type 1; Diabetic striatopathy; hyperglycemia hemichorea hemiballismus pediatrics..