Autoimmune Markers in Primary Biliary Cholangitis

Clin Liver Dis. 2024 Feb;28(1):93-101. doi: 10.1016/j.cld.2023.07.002. Epub 2023 Aug 17.

Abstract

Primary biliary cholangitis (PBC) is a chronic cholestatic liver disease. The most common antibody associated with PBC is the anti-mitochondrial antibody (AMA), present in 90% to 95% of patients. For patients who are AMA-negative, novel biomarkers, such as antinuclear antibody-specific antibodies Sp100 and gp210 and anti-kelch-like-12 and anti-hexokinase-1 antibodies, may further aid in the diagnosis of PBC. Several laboratory methods, including immunofluorescence, enzyme-linked immunosorbent assay, immunoblotting, and bead-based assays, exist to evaluate for the presence of antibodies. This article describes various methods used to evaluate antibodies as well as describe the antibodies present in PBC.

Keywords: AMA; ANA; Anti-mitochondrial antibody; Antinuclear antibody; Primary biliary cholangitis; Sp100; gp210.

Publication types

  • Review

MeSH terms

  • Antibodies, Antinuclear
  • Autoantibodies
  • Biomarkers
  • Cholangitis* / diagnosis
  • Cholestasis*
  • Humans
  • Liver Cirrhosis, Biliary* / diagnosis

Substances

  • Autoantibodies
  • Antibodies, Antinuclear
  • Biomarkers