Idiopathic interstitial pneumonia in a patient with von Hippel-Lindau syndrome: a first case

Letizia Corinna Morlacchi; Umberto Zanini; Andrea Gramegna; Paola Faverio; Francesco Blasi; Fabrizio Luppi

doi:10.1183/23120541.00504-2023

Idiopathic interstitial pneumonia in a patient with von Hippel-Lindau syndrome: a first case

ERJ Open Res. 2023 Nov 27;9(6):00504-2023. doi: 10.1183/23120541.00504-2023. eCollection 2023 Nov.

Authors

Letizia Corinna Morlacchi^{1

2

3}, Umberto Zanini^{4

5

3}, Andrea Gramegna^{1

2}, Paola Faverio^{4

5}, Francesco Blasi^{1

2}, Fabrizio Luppi^{4

5}

Affiliations

¹ Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.
² Internal Medicine Department, Respiratory Unit and Cystic Fibrosis Center, Fondazione IRCCS Cà Granda Ospedale Maggiore Policlinico, Milan, Italy.
³ These authors contributed equally.
⁴ UOC Pneumologia, Fondazione IRCCS San Gerardo dei Tintori, Monza, Italy.
⁵ School of Medicine and Surgery, University of Milano Bicocca, Milan, Italy.

Abstract

Although the mechanisms are not known, this is a case of progressive interstitial lung involvement, with a NSIP radiological pattern, evolving in pulmonary fibrosis in a patient with von Hippel-Lindau syndrome, without extrapulmonary fibrosis. https://bit.ly/3QlNStu.