Massive Right Ventricle Enlargement in Unrepaired Sinus Venosus Atrial Septal Defect: Repair or Not?

Carlo Mannina; Kali Hopkins; Barry Love; Ali N Zaidi

doi:10.1016/j.jaccas.2023.102091

Massive Right Ventricle Enlargement in Unrepaired Sinus Venosus Atrial Septal Defect: Repair or Not?

JACC Case Rep. 2023 Oct 27:28:102091. doi: 10.1016/j.jaccas.2023.102091. eCollection 2023 Dec 20.

Authors

Carlo Mannina¹, Kali Hopkins², Barry Love², Ali N Zaidi²

Affiliations

¹ Department of Medicine, Icahn School of Medicine at Mount Sinai, Mount Sinai Beth Israel, New York, New York, USA.
² Mount Sinai Heart, Icahn School of Medicine at Mount Sinai, New York, New York, USA.

Abstract

Sinus venosus atrial septal defect (SVASD) with partial anomalous pulmonary venous return is a rare congenital heart defect that may present in adulthood when right heart enlargement has already occurred. We describe a case of unrepaired sinus venosus atrial septal defect and partial anomalous pulmonary venous return with massive right heart enlargement and recurrent atrial arrhythmias.

Keywords: atrial arrhythmias; atrial septal defect; multimodality imaging; right ventricle.

Publication types

Case Reports