Clonal Dynamics and Relapse Risk Revealed by High-Sensitivity FLT3-Internal Tandem Duplication Detection in Acute Myeloid Leukemia

Mod Pathol. 2024 Sep;37(9):100534. doi: 10.1016/j.modpat.2024.100534. Epub 2024 Jun 7.

Abstract

The ability to detect low-level disease is key to our understanding of clonal heterogeneity in acute myeloid leukemia (AML) and residual disease that elude conventional assays and seed relapse. We developed a high-sensitivity next-generation sequencing (HS-NGS) clinical assay, able to reliably detect low levels (1 × 10-5) of FLT3-ITD, a frequent, therapeutically targetable and prognostically relevant mutation in AML. By applying this assay to 289 longitudinal samples from 62 patients at initial diagnosis and/or clinical follow-up (mean follow-up of 22 months), we reveal the frequent occurrence of FLT3-ITD subclones at diagnosis and demonstrate a significantly decreased relapse risk when FLT3-ITD is cleared after induction or thereafter. We perform pairwise sequencing of diagnosis and relapse samples from 23 patients to uncover more detailed patterns of FLT3-ITD clonal evolution at relapse than is detectable by less-sensitive assays. Finally, we show that rising ITD level during consecutive biopsies is a harbinger of impending relapse. Our findings corroborate the emerging clinical utility of high-sensitivity FLT3-ITD testing and expands our understanding of clonal dynamics in FLT3-ITD-positive AML.

Keywords: FLT3 internal tandem duplication; acute myeloid leukemia; clonal dynamics; high-sensitivity next-generation sequencing; measurable residual disease.

MeSH terms

  • Adult
  • Aged
  • Clonal Evolution
  • Female
  • Gene Duplication
  • High-Throughput Nucleotide Sequencing*
  • Humans
  • Leukemia, Myeloid, Acute* / genetics
  • Leukemia, Myeloid, Acute* / pathology
  • Male
  • Middle Aged
  • Mutation
  • Recurrence
  • Tandem Repeat Sequences / genetics
  • fms-Like Tyrosine Kinase 3* / genetics

Substances

  • fms-Like Tyrosine Kinase 3
  • FLT3 protein, human