Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child

Ramyasree Bade; Nitin James Peters; Joseph L Mathew; Indu Mohini Sen; Jai K Mahajan

doi:10.4103/jiaps.jiaps_1_24

Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child

J Indian Assoc Pediatr Surg. 2024 Jul-Aug;29(4):376-378. doi: 10.4103/jiaps.jiaps_1_24. Epub 2024 Jul 6.

Authors

Ramyasree Bade¹, Nitin James Peters¹, Joseph L Mathew², Indu Mohini Sen³, Jai K Mahajan¹

Affiliations

¹ Department of Pediatric Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
² Department of Pediatrics, Pediatric Pulmonology Unit, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
³ Department of Anesthesia and Critical Care, Division of Pediatric Anesthesia, Post Graduate Institute of Medical Education and Research, Chandigarh, India.

Abstract

Congenital extrahepatic portosystemic shunts (CEPS) are rare anomalies connecting the portal system to the inferior vena cava. This report discusses a 10-year-old boy with Type II c CEPS, presenting cyanosis and dyspnea. Surgical ligation resulted in significant improvement in symptoms. Early identification and intervention are crucial, necessitating a protocolized approach.

Keywords: Central cyanosis; congenital extrahepatic portosystemic shunt; surgical ligation.

Publication types

Case Reports