A challenging case presentation of multiple system atrophy cerebellar type: A rare case report from Somalia

Radiol Case Rep. 2024 Sep 23;19(12):6183-6186. doi: 10.1016/j.radcr.2024.08.145. eCollection 2024 Dec.

Abstract

Multiple system atrophy is a rare and quickly progressing neurological condition characterized by autonomic failure, parkinsonism, or cerebellar ataxia. It is classified into two subtypes: MSA with predominant parkinsonism (MSA-P) and MSA with predominant cerebellar ataxia (MSA-C). We are presenting here a 54-year-old male with parkinsonism, ataxia, and dysarthria. He was diagnosed with parkinson disease and was given a maximum dose of levodopa but has not responded. After a close neurological evaluation with magnetic resonance imaging of the brain, which shows atrophy of the cerebellum and a brainstem with a hot cross bun sign of the pons, suggestive of multiple system atrophy, he was diagnosed with multiple system atrophy cerebellar type, which is the first time to have this diagnosis in Somalia, which is a low-resource country.

Keywords: Ataxia; Atrophy; Cerebellum; Multiple system atrophy; Parkinsonism.

Publication types

  • Case Reports