Conserved region of human TDP-43 is structurally similar to membrane binding protein FARP1 and protein chaperons BAG6 and CYP33

MicroPubl Biol. 2024 Nov 7:2024:10.17912/micropub.biology.001388. doi: 10.17912/micropub.biology.001388. eCollection 2024.

Abstract

Transactive response DNA-binding protein of 43 KDa (TDP-43) is important for RNA metabolism in all animals and in humans is involved in neuromuscular diseases. Full-length TDP-43 is prone to oligomerization and misfolding what renders difficult its characterization. We report that TDP-43 domains are structurally similar to lipid binding protein FARP1 and protein chaperons BAG6 and CYP33. Sequence analysis suggests putative lipid binding sites throughout TDP-43 and in vitro thioflavin T fluorescence assays show that cholesterol and phosphatidylcholine affect fibrillation of recombinant TDP-43 fragments. Our findings suggest that TDP-43 can bind lipids directly and it may contribute to its own chaperoning.

Grants and funding

This work was supported by an Arturo Falaschi ICGEB fellowship (Lj. S.) and grants NOSRESCUE ALS (AriSLA) (E. B.).