Tibiopelvic Rotational Arthroplasty for Pediatric Gorham-Stout Disease: A Case Report and Surgical Technique

JBJS Case Connect. 2024 Dec 5;14(4). doi: 10.2106/JBJS.CC.24.00172. eCollection 2024 Oct 1.

Abstract

Case: This is a case of a 6-year-old patient diagnosed with Gorham-Stout disease (GSD), a rare lymphangiogenic skeletal disorder, localized to the left femur. Initial nonoperative treatment with pharmaceuticals and bracing was unsuccessful. We describe a definitive operative treatment with radical femoral resection and a modified rotationplasty technique through a tibiopelvic rotational hip arthroplasty. At 2-year follow-up, the patient was able to walk with a prosthetic device.

Conclusion: The use of this modified rotationplasty technique is an effective treatment option for patients with femoral GSD to improve function and quality of life.

Publication types

  • Case Reports

MeSH terms

  • Arthroplasty, Replacement, Hip / methods
  • Child
  • Humans
  • Osteolysis, Essential* / diagnostic imaging
  • Osteolysis, Essential* / surgery