Total Hip Replacement in a Patient with Erdheim-Chester's Disease: A Case Report

JBJS Case Connect. 2024 Dec 12;14(4). doi: 10.2106/JBJS.CC.20.01021. eCollection 2024 Oct 1.

Abstract

Case: Erdheim-Chester's disease (ECD) is a rare multisystem disorder considered as a neoplasm of non-Langerhans cell histiocytes. We report a case of uncemented total hip arthroplasty in a 74-year-old patient with ECD for femoral neck fracture with pathological involvement of distal metaphysis and diaphysis. We reviewed the literature on bony involvement.

Conclusion: Adequate osseointegration was achieved in our case; however, longer follow-up is essential. Vigilant reporting of bony involvement, such as pathological fractures, fracture healing, deformities, osteosynthesis, and outcome of joint replacement surgeries, is needed in ECD-like bone diseases.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aged
  • Arthroplasty, Replacement, Hip*
  • Erdheim-Chester Disease* / complications
  • Erdheim-Chester Disease* / diagnostic imaging
  • Erdheim-Chester Disease* / surgery
  • Femoral Neck Fractures / diagnostic imaging
  • Femoral Neck Fractures / surgery
  • Humans