Pediatric Retroperitoneal Paraganglioma Invading the Inferior Vena Cava: A Case Report and Literature Review

J Nippon Med Sch. 2024;91(6):554-559. doi: 10.1272/jnms.JNMS.2024_91-603.

Abstract

Paraganglioma, a catecholamine-producing tumor originating in extra-adrenal paraganglion cells, is rare in children. Although diagnosis of paraganglioma is based on the presence of catecholamine symptoms, some patients lack such symptoms. Delayed diagnosis is associated with tumor growth and invasion of surrounding vessels. Herein, we report a case of pediatric retroperitoneal paraganglioma invading the inferior vena cava. The tumor was completely resected and the patient has been free of recurrence for 2 years. Our findings suggest that complete resection can help prevent recurrence in cases of invasion of the inferior vena cava.

Keywords: invasion; pediatric surgery; retroperitoneal paraganglioma.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Child
  • Female
  • Humans
  • Male
  • Neoplasm Invasiveness*
  • Paraganglioma* / diagnostic imaging
  • Paraganglioma* / pathology
  • Paraganglioma* / surgery
  • Retroperitoneal Neoplasms* / diagnostic imaging
  • Retroperitoneal Neoplasms* / pathology
  • Retroperitoneal Neoplasms* / surgery
  • Tomography, X-Ray Computed
  • Treatment Outcome
  • Vena Cava, Inferior* / pathology