Perifollicular fibroma is a very unusual lesion and infrequently seen. The present report describes a thirty-two year old white man with unusual manifestations of this condition which usually presents as a small number of lesions on the head and neck, most often in adults. It has a characteristic pathologic picture of perifollicular fibrosis. The origin of this lesion is uncertain, but most probably represents a tumor of the connective tissue sheath of the follicle.