Cholestanolosis (cerebrotendinous xanthomatosis). A follow-up study on the original family

Arch Neurol. 1969 Dec;21(6):603-10. doi: 10.1001/archneur.1969.00480180059004.
No abstract available

MeSH terms

  • Adult
  • Age Factors
  • Brain / pathology
  • Cataract / genetics*
  • Cerebellar Ataxia / etiology
  • Cerebellar Diseases / genetics*
  • Cerebellar Diseases / pathology
  • Cerebellum / pathology
  • Child
  • Cholestanes / blood
  • Cholestanes / metabolism*
  • Female
  • Follow-Up Studies
  • Humans
  • Intellectual Disability / etiology
  • Lipid Metabolism, Inborn Errors* / pathology
  • Spinal Cord / pathology
  • Spinal Cord Diseases / etiology
  • Xanthomatosis / etiology
  • Xanthomatosis / genetics*
  • Xanthomatosis / pathology

Substances

  • Cholestanes