A 17-year-old boy with spastic quadriplegia presented with a progressively enlarging, tender, right inguinal mass. Examination revealed absence of both testicles in the scrotal sac. The left testicle was palpable in the left superficial inguinal pouch. A diagnosis of an undescended right testicle was confirmed by exploratory surgery. Orchidectomy of the right testicle was performed and the remainder of the patient's course was uneventful. We present this case to describe the relationship between cryptorchidism, testicular torsion, and neuromuscular disease. Specific emphasis is placed on incidence, pathophysiological mechanisms, and treatment of testicular torsion in cryptorchidism.