Eosinophilic fasciitis

JAMA. 1978 Aug 4;240(5):451-3.

Abstract

Shulman's syndrome includes fasciitis of rapid onset, sclerodermoid skin changes, absence of Raynaud's phenomenon, absence of visceral manifestations of progressive systemic sclerosis, hypergammaglobulinemia, transient eosinophilia, and a dramatic response to systemic corticosteroid therapy. Although this syndrome may be a variant of scleroderma, its dramatic responsiveness to corticosteroid therapy is a particularly distinguishing feature.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Diagnosis, Differential
  • Eosinophilia / complications*
  • Eosinophilia / drug therapy
  • Fascia* / pathology
  • Female
  • Humans
  • Hypergammaglobulinemia / complications*
  • Inflammation / complications
  • Inflammation / drug therapy
  • Male
  • Middle Aged
  • Prednisone / therapeutic use
  • Scleroderma, Systemic / diagnosis
  • Skin Manifestations
  • Syndrome

Substances

  • Prednisone