[Athymhormic syndrome and progressive paraplegia disclosing adrenoleukomyeloneuropathy in an adult]

Rev Neurol (Paris). 1995 Jun-Jul;151(6-7):388-91.
[Article in French]

Abstract

A 40-year-old man presented with both paraparesia and an athymhormic syndrome. Bicapsular lesions together with abnormal evoked motor potentials suggested cortical and spinal involvement in the deficiency syndrome. The neuropsychologic symptoms appeared to be secondary to bilateral pallidium lesions. Associated signs were adrenoleukocystrophy and adrenomyeloneuropathy suggesting the term, adrenoleukocyeloneuropathy.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adrenoleukodystrophy / complications
  • Adrenoleukodystrophy / diagnosis*
  • Adrenoleukodystrophy / physiopathology
  • Adult
  • Electromyography
  • Evoked Potentials
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Paraplegia / etiology*
  • Paraplegia / physiopathology
  • Psychomotor Disorders / etiology*
  • Psychomotor Disorders / physiopathology