Polymerization of recombinant Hb S-Kempsey (deoxy-R state) and Hb S-Kansas (oxy-T state)

J Biol Chem. 1995 Nov 10;270(45):26857-62. doi: 10.1074/jbc.270.45.26857.

Abstract

In order to investigate the role of the R (relaxed) to T (tense) structural transition in facilitating polymerization of deoxy-Hb S, we have engineered and expressed two Hb S variants which destabilize either T state (Hb S-Kempsey, alpha 2 beta 2 Val-6,Asn-99) or R state structures (Hb S-Kansas, alpha 2 beta 2 Val-6, Thr-102). Polymerization of deoxy-Hb S-Kempsey, which shows high oxygen affinity and increased dimer dissociation, required about 2- and 6-fold higher hemoglobin concentrations than deoxy-Hb S for polymerization in low and high phosphate concentrations, and its kinetic pattern of polymerization was biphasic. In contrast, oxy- or CO Hb S-Kansas, which shows low oxygen affinity and increased dimer dissociation, polymerized at a slightly higher critical concentration than that required for polymerization of deoxy-Hb S in both low and high phosphate buffers. Polymerization of oxy- and CO Hb S-Kansas was linear and showed no delay time, which is similar to oversaturated oxy- or CO Hb S. These results suggest that nuclei formation, which occurs during the delay time prior to deoxy-Hb S polymerization, does not occur in T state oxy-Hb S-Kansas, even though the critical concentration for polymerization of T state oxy-Hb S-Kansas is similar to that of T state deoxy-Hb S.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Carboxyhemoglobin / chemistry
  • Carboxyhemoglobin / genetics
  • Genetic Variation
  • Hemoglobins / chemistry
  • Hemoglobins / genetics
  • Hemoglobins, Abnormal / chemistry*
  • Hemoglobins, Abnormal / genetics
  • Humans
  • Kinetics
  • Molecular Structure
  • Oxidation-Reduction
  • Oxyhemoglobins / chemistry
  • Oxyhemoglobins / genetics
  • Polymers / chemistry
  • Protein Conformation
  • Recombinant Proteins / chemistry
  • Recombinant Proteins / genetics
  • Saccharomyces cerevisiae / genetics

Substances

  • Hemoglobins
  • Hemoglobins, Abnormal
  • Oxyhemoglobins
  • Polymers
  • Recombinant Proteins
  • hemoglobin Kempsey
  • deoxyhemoglobin
  • hemoglobin Kansas
  • Carboxyhemoglobin