Craniopharyngioma: endocrine abnormalities at presentation

Pediatr Neurosurg. 1994:21 Suppl 1:18-20. doi: 10.1159/000120856.

Abstract

Craniopharyngioma is the most common childhood tumor to involve the hypothalamus and pituitary. Although endocrine disturbances can be found in 80-90% of patients at presentation, only a minority of subjects seek medical attention for an endocrine-related complaint. Hormonal studies, while limited, indicate GH deficiency in 75% of children; deficiencies of LH/FSH (40%), ACTH (25%) and TSH (25%) also are common. In contrast, diabetes insipidus has been noted in only 9-17% of subjects prior to surgery. When possible, full evaluation of pituitary function should be performed; the minimum preoperative evaluation must include testing for and treatment of ACTH-adrenal insufficiency and diabetes insipidus.

Publication types

  • Review

MeSH terms

  • Adrenal Insufficiency / blood
  • Adrenal Insufficiency / diagnosis
  • Adrenal Insufficiency / surgery
  • Child
  • Craniopharyngioma / blood
  • Craniopharyngioma / diagnosis*
  • Craniopharyngioma / surgery
  • Diabetes Insipidus / blood
  • Diabetes Insipidus / diagnosis
  • Diabetes Insipidus / surgery
  • Humans
  • Paraneoplastic Endocrine Syndromes / blood
  • Paraneoplastic Endocrine Syndromes / diagnosis*
  • Paraneoplastic Endocrine Syndromes / surgery
  • Pituitary Function Tests
  • Pituitary Hormones / blood
  • Pituitary Neoplasms / blood
  • Pituitary Neoplasms / diagnosis*
  • Pituitary Neoplasms / surgery

Substances

  • Pituitary Hormones