Bilateral large-cell calcifying Sertoli cell tumor of the testes with Peutz-Jeghers syndrome: a case report

Pediatr Dermatol. 1994 Dec;11(4):335-7. doi: 10.1111/j.1525-1470.1994.tb00100.x.

Abstract

A 13-year-old boy with Peutz-Jeghers syndrome (PJs), gynecomastia, and bilateral multifocal testicular tumors is described. Histology of the testicular tissue disclosed large-cell calcifying Sertoli cell tumors. Females with PJs are known to be at increased risk of developing gonadal tumors. This case and a review of other reported cases suggest that males with PJs are also at risk for developing gonadal tumors.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adolescent
  • Biopsy
  • Child
  • Child, Preschool
  • Gynecomastia / complications
  • Humans
  • Male
  • Neoplasms, Multiple Primary / complications
  • Neoplasms, Multiple Primary / pathology*
  • Orchiectomy
  • Peutz-Jeghers Syndrome / complications*
  • Sertoli Cell Tumor / complications*
  • Sertoli Cell Tumor / diagnostic imaging
  • Sertoli Cell Tumor / pathology*
  • Sertoli Cell Tumor / surgery
  • Testicular Neoplasms / complications*
  • Testicular Neoplasms / diagnostic imaging
  • Testicular Neoplasms / pathology*
  • Testicular Neoplasms / surgery
  • Ultrasonography