[Relationships between rhizomelic pseudo-polyarthritis and mitochondrial myopathy. 24 cases]

Presse Med. 1994 Jan;23(1):15-8.
[Article in French]

Abstract

Objectives: Diagnosis of polymyalgia rheumatica requires the elimination of other inflammatory diseases due to the lack of a specific diagnostic criteria. Since results of muscle biopsy have been considered non-specific, we evaluated the full spectrum of histological, histochemical and biochemical data observed in 24 patients with suspected polymyalgia rheumatica.

Methods: From January 1989, the diagnosis of polymyalgia rheumatica was suspected in 24 patients (4 males, 20 females; mean age 67.8 years, range 50-88) hospitalized in our unit for inflammatory joint and muscle pain with a current duration of 6-30 months. Muscle biopsies were obtained in each case.

Results: Based on the histological, histo-enzymatic, ultrastructural and biochemical analyses, 19 patients fulfilled the criteria defining mitochondrial myopathies. After favourable outcome (reduced pain, involution of biochemical inflammatory syndrome) following prednisone therapy (0.5 mg/kg/day) a second muscle biopsy revealed identical abnormalities.

Conclusion: These muscular diseases have been described mainly as hereditary encephalo-myopathies, but in our series the mitochondrial myopathy may have preceded the polymyalgia rheumatica or been acquired, aggravating the inflammatory process. Muscle biopsy might act as a referee for diagnosis.

MeSH terms

  • Aged
  • Aged, 80 and over
  • Biopsy
  • Cytochrome-c Oxidase Deficiency
  • Diagnosis, Differential
  • Electron Transport Complex III / deficiency
  • Female
  • Humans
  • Male
  • Microscopy, Electron
  • Middle Aged
  • Mitochondrial Myopathies / complications
  • Mitochondrial Myopathies / pathology*
  • NAD(P)H Dehydrogenase (Quinone) / deficiency
  • Polymyalgia Rheumatica / complications
  • Polymyalgia Rheumatica / drug therapy
  • Polymyalgia Rheumatica / enzymology
  • Polymyalgia Rheumatica / pathology*
  • Prednisone / therapeutic use

Substances

  • NAD(P)H Dehydrogenase (Quinone)
  • Electron Transport Complex III
  • Prednisone