[Chronic urticaria-macroglobulinemia (Schnitzler syndrome): developing to IgM myeloma. Apropos of a case]

Rev Med Interne. 1993;14(8):780-3. doi: 10.1016/s0248-8663(05)81424-9.
[Article in French]

Abstract

Schnitzler's syndrome has been described in 1972. It associates a chronic urticaria with leukocytoclastic vasculitis, a macroglobulinemia, bone pains, hyperostosis. In the twenty three cases reported, the evolution is benign but three patients including the princeps case developed a Waldenström's disease or a lymphoplasmocytic lymphoma. We present the case of one patient, aged 65, with Schnitzler's syndrome, who, after 6 years evolution, presents a IgM myeloma. Schnitzler's syndrome appeared as a pre-hemopathic state which has to be taken care of regularly and for a long time.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Aged
  • Chlorambucil / therapeutic use
  • Chronic Disease
  • Humans
  • Immunoglobulin M*
  • Male
  • Multiple Myeloma / drug therapy
  • Multiple Myeloma / etiology*
  • Syndrome
  • Time Factors
  • Urticaria / complications*
  • Urticaria / drug therapy
  • Urticaria / physiopathology
  • Waldenstrom Macroglobulinemia / complications*
  • Waldenstrom Macroglobulinemia / drug therapy
  • Waldenstrom Macroglobulinemia / physiopathology

Substances

  • Adrenal Cortex Hormones
  • Immunoglobulin M
  • Chlorambucil