We present the case of a 27-year-old woman with a vascular malformation localized in the superior orbital fissure. Histological diagnosis was that of a venous angioma with papillary endothelial hyperplasia. The lesion was removed completely via an intradural approach to the superior orbital fissure with subsequent recovery of the neurological deficits. To the best of our knowledge, no such case has been reported so far in the literature. The radiological, intraoperative, and histopathological findings are presented and discussed with respect to the literature.