Localization of the chromosome 15 breakpoints and expression of multiple PML-RAR alpha transcripts in acute promyelocytic leukemia: a study of 28 Chinese patients

Leukemia. 1993 Jan;7(1):20-6.

Abstract

Translocation (15;17)(q22;q12-q21) is a chromosome aberration specifically found in acute promyelocytic leukemia (APL), that generates a chimeric gene between the promyelocytic leukemia (PML) gene on chromosome 15 and the retinoic acid receptor alpha (RARA) gene, on chromosome 17. In the course of molecular investigations of a series of 28 Chinese patients with APL, we have simultaneously used Southern blot and reverse transcriptase polymerase chain reaction (RT-PCR) analysis to characterize the PML gene breakpoints on chromosome 15 and identify PML-RARA fusion transcripts. Our results confirmed the existence of the three recently described bcr1, bcr2, and bcr3 breakpoint cluster regions. In addition, structural data provided by PML-RARA transcripts allowed us to more accurately locate the 3' borders of clusters bcr1 and bcr3. Moreover, our data suggest a preferential localization of the breakpoints within bcr1 and bcr3. The primary structure of a 1.4 kb DNA segment flanking the 5' part of the PML gene and that of the bcr3 cluster (2.1 kb) were also established.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Base Sequence
  • Carrier Proteins / genetics*
  • China / ethnology
  • Chromosomes, Human, Pair 15*
  • Chromosomes, Human, Pair 17
  • DNA, Neoplasm / genetics
  • Gene Expression
  • Genes
  • Humans
  • Leukemia, Promyelocytic, Acute / genetics*
  • Molecular Sequence Data
  • Neoplasm Proteins*
  • Nuclear Proteins*
  • Promyelocytic Leukemia Protein
  • Protein-Tyrosine Kinases*
  • Proto-Oncogene Proteins / genetics
  • Proto-Oncogene Proteins c-bcr
  • RNA, Messenger / genetics
  • RNA, Neoplasm / genetics
  • Receptors, Retinoic Acid
  • Regulatory Sequences, Nucleic Acid
  • Restriction Mapping
  • Transcription Factors / genetics*
  • Translocation, Genetic
  • Tumor Suppressor Proteins

Substances

  • Carrier Proteins
  • DNA, Neoplasm
  • Neoplasm Proteins
  • Nuclear Proteins
  • Promyelocytic Leukemia Protein
  • Proto-Oncogene Proteins
  • RNA, Messenger
  • RNA, Neoplasm
  • Receptors, Retinoic Acid
  • Transcription Factors
  • Tumor Suppressor Proteins
  • PML protein, human
  • Protein-Tyrosine Kinases
  • BCR protein, human
  • Proto-Oncogene Proteins c-bcr