Dermatitis in treated maple syrup urine disease

J Am Acad Dermatol. 1993 Feb;28(2 Pt 2):289-92. doi: 10.1016/0190-9622(93)70036-s.

Abstract

Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Dermatitis / drug therapy
  • Dermatitis / etiology*
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Isoleucine / administration & dosage
  • Isoleucine / blood
  • Leucine / administration & dosage
  • Leucine / blood
  • Maple Syrup Urine Disease / complications*
  • Maple Syrup Urine Disease / diet therapy
  • Recurrence

Substances

  • Isoleucine
  • Leucine