Two patients with complete duplex kidney accompanied by ectopic ureterocele and vesicoureteral reflux (VUR) had repeated episodes of refractory urinary tract infection. One patient was a 11-year-old girl who showed VUR into the cele ureter. The other patient was a 17-year-old female who showed VUR into the mate ureter. Satisfactory results could be obtained by twin ureteroneocystomy with cele wall resection in both cases. Complete duplex kidney is often complicated by urinary tract abnormalities such as ectopic ureterocele, VUR, and renal dysplasia, and these complications complicate its diagnosis. The treatment of complete duplex kidney with urinary tract abnormalities are discussed.