YAC and cosmid contigs spanning the Batten disease (CLN3) region at 16p12.1-p11.2

Genomics. 1995 Sep 20;29(2):478-89. doi: 10.1006/geno.1995.9978.

Abstract

A yeast artificial chromosome (YAC) contig has been constructed in 16p12.1-p11.2 that encompasses three loci (D16S288, D16S299, and D16S298) closely linked to the gene causing Batten disease or juvenile-onset neuronal ceroid lipofuscinosis (CLN3). The physical map has been ordered using 42 sequence tagged sites. Four genes, interleukin-4 receptor (IL4R), phenol-preferring phenol sulfotransferase (STP), monoamine-preferring phenol sulfotransferase (STM), and sialophorin (SPN), have been mapped to the YAC contig. A partial genomic restriction map has been constructed to confirm the order and distances between D16S298, predicted to be the locus closest to CLN3. The overlapping genomic clones are a valuable resource for cloning the Batten gene (CLN3) and other genes in the region.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Antigens, CD / genetics
  • Arylsulfotransferase / genetics
  • Base Sequence
  • Chromosome Mapping
  • Chromosomes, Artificial, Yeast
  • Chromosomes, Human, Pair 16*
  • Cosmids
  • DNA Primers
  • Genetic Linkage
  • Genetic Markers
  • Humans
  • In Situ Hybridization, Fluorescence
  • Interleukin-4 / metabolism
  • Isoenzymes / genetics
  • Leukosialin
  • Molecular Sequence Data
  • Neuronal Ceroid-Lipofuscinoses / genetics*
  • Polymerase Chain Reaction / methods
  • Receptors, Interleukin / genetics
  • Receptors, Interleukin-4
  • Restriction Mapping
  • Sequence Tagged Sites
  • Sialoglycoproteins / genetics

Substances

  • Antigens, CD
  • DNA Primers
  • Genetic Markers
  • Isoenzymes
  • Leukosialin
  • Receptors, Interleukin
  • Receptors, Interleukin-4
  • SPN protein, human
  • Sialoglycoproteins
  • Interleukin-4
  • Arylsulfotransferase