Multiple inflammatory fibrosarcoma of the abdominal cavity in a child

Med Pediatr Oncol. 1996 Sep;27(3):198-201. doi: 10.1002/(SICI)1096-911X(199609)27:3<198::AID-MPO12>3.0.CO;2-C.

Abstract

Inflammatory fibrosarcoma is a rare condition in childhood. In the abdominal location, its behaviour is often aggressive and potentially metastasizing. We report a case of a 3-year-old female with abdominal inflammatory fibrosarcoma who relapsed after 1 month from radical surgery. Chemotherapy was ineffective, and we registered a brief stabilisation of disease only with alpha-IFN. Our case confirms the potential malignancy of this tumour and its resistance to treatment. It is noteworthy that the therapy with alpha-IFN improved the quality of life in this child for 4 months.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abdominal Neoplasms* / diagnosis
  • Abdominal Neoplasms* / pathology
  • Abdominal Neoplasms* / therapy
  • Child, Preschool
  • Female
  • Fibrosarcoma* / diagnosis
  • Fibrosarcoma* / pathology
  • Fibrosarcoma* / therapy
  • Humans
  • Interferon-alpha / therapeutic use
  • Neoplasms, Multiple Primary* / pathology

Substances

  • Interferon-alpha