Fibrillin-1 and fibulin-2 interact and are colocalized in some tissues

J Biol Chem. 1996 Aug 9;271(32):19489-96. doi: 10.1074/jbc.271.32.19489.

Abstract

Microfibrils 10-12 nm in diameter are found in elastic and non-elastic tissues with fibrillin as a major component. Little is known about the supramolecular structure of these microfibrils and the protein interactions it is based on. To identify protein binding ligands of fibrillin-1, we tested binding of recombinant fibrillin-1 peptides to different extracellular matrix proteins in solid phase assays. Among the proteins tested, only fibulin-2 showed significant binding to rF11, the N-terminal half of fibrillin-1, in a calcium-dependent manner. Surface plasmon resonance demonstrated high affinity binding with a Kd = 56 nM. With overlapping recombinant fibrillin-1 peptides, the binding site for fibulin-2 was narrowed down to the N terminus of fibrillin-1 (amino acid positions 45-450). Immunofluorescence in tissues demonstrated colocalization of fibrillin and fibulin-2 in skin, perichondrium, elastic intima of blood vessels, and kidney glomerulus. Fibulin-2 was not present in ocular ciliary zonules, tendon, and the connective tissue around kidney tubules and lung alveoli, which all contain fibrillin. Immunogold labeling of fibulin-2 on microfibrils in skin was found preferentially at the interface between microfibrils and the amorphous elastin core, suggesting that in vivo the interaction between fibrillin-1 and fibulin-2 is regulated by cellular expression and deposition as well as by protein-protein interactions.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Base Sequence
  • Calcium-Binding Proteins / metabolism*
  • Cattle
  • Child
  • DNA Primers
  • Extracellular Matrix Proteins / metabolism*
  • Fibrillin-1
  • Fibrillins
  • Humans
  • Kinetics
  • Male
  • Mice
  • Microfilament Proteins / metabolism*
  • Microscopy, Immunoelectron
  • Molecular Sequence Data
  • Protein Binding
  • Recombinant Proteins / metabolism
  • Skin / metabolism
  • Skin / ultrastructure
  • Species Specificity

Substances

  • Calcium-Binding Proteins
  • DNA Primers
  • Extracellular Matrix Proteins
  • FBN1 protein, human
  • Fbn1 protein, mouse
  • Fibrillin-1
  • Fibrillins
  • Microfilament Proteins
  • Recombinant Proteins
  • fibulin 2