Abstract
We report the findings in a child with the Denys-Drash syndrome presenting prenatally with a diaphragmatic hernia, male pseudohermaphroditism, and elevated alpha-fetoprotein levels i amniotic fluid and in maternal serum.
MeSH terms
-
Amniocentesis
-
Amniotic Fluid / chemistry*
-
Disorders of Sex Development / genetics
-
Fatal Outcome
-
Female
-
Fetal Diseases / diagnosis*
-
Fetal Diseases / embryology
-
Fetal Diseases / genetics
-
Gestational Age
-
Hernia, Diaphragmatic / diagnostic imaging
-
Hernia, Diaphragmatic / embryology
-
Humans
-
Infant, Newborn
-
Kidney Neoplasms / genetics
-
Male
-
Nephrotic Syndrome / diagnosis*
-
Nephrotic Syndrome / embryology
-
Nephrotic Syndrome / genetics
-
Point Mutation / genetics
-
Pregnancy
-
Prenatal Diagnosis*
-
Ultrasonography, Prenatal
-
Wilms Tumor / genetics
-
alpha-Fetoproteins / analysis*