Assembly of the cardiac I-band region of titin/connectin: expression of the cardiac-specific regions and their structural relation to the elastic segments

J Muscle Res Cell Motil. 1996 Aug;17(4):449-61. doi: 10.1007/BF00123361.

Abstract

The giant molecule titin (also called connectin) provides an elastic connection in the I-band between the Z-disk and A-band of striated muscle. This region is assembled in a tissue-specific way by extensive differential splicing events. We have raised monoclonal antibodies against the two N2-line isoforms of titin and demonstrate that both forms of cardiac I-band titin are constitutively co-expressed in atrial and ventricular muscle. In developing mouse embryos, the expression of the cardiac N2-B isoform remains strictly cardiac-specific and is linked to the expression of the ubiquitous N2-A isoform. The mechanical function of the cardiac N2-line region was investigated ultrastructurally. Immunoelectron microscopy reveals that the N2-B region separates two mechanically distinct sections of titin with a hyperextensible segment spanning the distance to the Z-disk. The formation of a plateau in the extension of cardiac titin rules out that Ig-domains can be unfolded as a mechanism of elasticity.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Calmodulin-Binding Proteins / metabolism*
  • Carrier Proteins / metabolism*
  • Connectin
  • Fluorescent Antibody Technique, Indirect
  • Humans
  • Membrane Proteins / metabolism*
  • Mice
  • Microscopy, Immunoelectron
  • Muscle Proteins / metabolism*
  • Myocardium / metabolism*
  • Polymerase Chain Reaction
  • Protein Kinases / metabolism*
  • Sarcomeres / metabolism

Substances

  • Calmodulin-Binding Proteins
  • Carrier Proteins
  • Connectin
  • Membrane Proteins
  • Muscle Proteins
  • TTN protein, human
  • Protein Kinases