Autism and the X chromosome. Multipoint sib-pair analysis

Arch Gen Psychiatry. 1996 Nov;53(11):985-9. doi: 10.1001/archpsyc.1996.01830110021003.

Abstract

Background: Genetic factors undoubtedly play a major etiologic role in autism, but how it is inherited remains unanswered. The increased incidence in males suggests possible involvement of the X chromosome.

Methods: Using data from 38 multiplex families with autism (2 or more autistic siblings), we performed a multipoint sib-pair linkage analysis between autism and 35 microsatellite markers located on the X chromosome. The model included a single parameter, the risk ratio lambda xs (i.e., ratio of risk to siblings compared with the population prevalence), owing to an X-linked gene. Different lambda xs values were assumed and regions of exclusion were established.

Results: The entire X chromosome could be excluded for a lambda xs value of 4. The ability to exclude an X-linked gene decreased with smaller lambda xs values, and some positive evidence was obtained with smaller values. A maximum lod score of 1.24 was obtained at locus DXS424 with a lambda xs value of 1.5.

Conclusions: We were able to exclude any moderate to strong gene effect causing autism on the X chromosome. Smaller gene effects (lambda xs < 4) could not be excluded, in particular, a gene of small effect located between DXS453 and DXS1001.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adolescent
  • Adult
  • Autistic Disorder / etiology
  • Autistic Disorder / genetics*
  • Chromosome Mapping
  • Family
  • Female
  • Genetic Markers
  • Genotype
  • Humans
  • Lod Score
  • Male
  • Microsatellite Repeats
  • Odds Ratio
  • X Chromosome / genetics*

Substances

  • Genetic Markers