T-cell-directed TAL-1 expression induces T-cell malignancies in transgenic mice

Cancer Res. 1996 Nov 15;56(22):5113-9.

Abstract

The TAL-1 gene specifies for a basic domain-helix-loop-helix protein, which is involved in the control of normal hematopoiesis. In human pathology, the TAL-1 gene product is expressed in a high percentage of T-cell acute lymphoblastic leukemias in the pediatric age range; however, it has not been established whether the expression has a causal role in oncogenesis. In this report, we describe the phenotype of mouse transgenic lines obtained by inducing tal-1 protein expression in lymphoid tissues using the LCK promoter. The survival rate of tal-1 transgenic animals was much lower as compared with control mice. Histopathological analysis revealed lymphomas of T-cell type, often comprising a minor B-cell component. Some mice showed marked splenic lymphocyte depletion. Primary lymphocyte cultures showed partial independence from exogenous growth stimuli and increased resistance to low-serum apoptosis. To further unravel the tal-1 oncogenic potential, a strain of tal-1 transgenic mice was crossbred with p53-/- mice; the survival rate in these animals was reduced by more than one-half when compared with that of tal-1 mice, and histopathological analysis revealed exclusively T-cell lymphomas. These data indicate that TAL-1, expressed in T cells, is per se a potent oncogene, which may exert a key leukemogenetic role in the majority of T-cell acute lymphoblastic leukemias.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adenovirus E2 Proteins / metabolism*
  • Animals
  • Basic Helix-Loop-Helix Transcription Factors
  • CD3 Complex / metabolism
  • DNA-Binding Proteins / genetics
  • DNA-Binding Proteins / metabolism*
  • Gene Deletion
  • Genes, p53 / genetics
  • Humans
  • Leukemia-Lymphoma, Adult T-Cell / genetics*
  • Leukemia-Lymphoma, Adult T-Cell / immunology
  • Leukemia-Lymphoma, Adult T-Cell / metabolism
  • Leukemia-Lymphoma, Adult T-Cell / mortality
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Oncogene Proteins, Fusion / metabolism*
  • Oncogenes / genetics
  • Oncogenes / physiology*
  • Phenotype
  • Proto-Oncogene Proteins*
  • RNA, Messenger / metabolism
  • Spleen / metabolism
  • T-Cell Acute Lymphocytic Leukemia Protein 1
  • T-Lymphocytes / metabolism*
  • Thymus Gland / metabolism
  • Transcription Factors / genetics
  • Transcription Factors / metabolism*

Substances

  • Adenovirus E2 Proteins
  • Basic Helix-Loop-Helix Transcription Factors
  • CD3 Complex
  • DNA-Binding Proteins
  • Oncogene Proteins, Fusion
  • Proto-Oncogene Proteins
  • RNA, Messenger
  • T-Cell Acute Lymphocytic Leukemia Protein 1
  • Tal1 protein, mouse
  • Transcription Factors
  • TAL1 protein, human