Primary cutaneous Langerhans cell histiocytosis treated with photochemotherapy

J Dermatol. 1997 Jan;24(1):54-6. doi: 10.1111/j.1346-8138.1997.tb02740.x.

Abstract

A 23-year-old man with Langerhans cell histiocytosis presented with asymptomatic, purplish, slightly scaly, confluent papules of one year's duration. Histological studies of biopsy specimens revealed a dense infiltrate of histiocytic mononuclear cells beneath the epidermis; these cells reacted strongly with anti-S-100 antibodies. Extensive investigations failed to detect systemic involvement. He was treated with repeated oral 8-methoxypsoralen (8-MOP) plus ultraviolet A (PUVA) therapy three times a week for two months and then once or twice with maintenance phototherapy. The lesions did not recur during the four-month follow-up period.

Publication types

  • Case Reports

MeSH terms

  • Administration, Oral
  • Adult
  • Epidermis / pathology
  • Follow-Up Studies
  • Histiocytes / pathology
  • Histiocytosis, Langerhans-Cell / drug therapy*
  • Histiocytosis, Langerhans-Cell / pathology
  • Humans
  • Male
  • Methoxsalen / administration & dosage
  • Methoxsalen / therapeutic use
  • PUVA Therapy*
  • Photosensitizing Agents / administration & dosage
  • Photosensitizing Agents / therapeutic use
  • S100 Proteins / analysis
  • Skin Diseases / drug therapy*
  • Skin Diseases / pathology

Substances

  • Photosensitizing Agents
  • S100 Proteins
  • Methoxsalen