Sonographic and maternal serum screening abnormalities in fetuses affected by spinal muscular atrophy

Prenat Diagn. 1997 Feb;17(2):166-9. doi: 10.1002/(sici)1097-0223(199702)17:2<166::aid-pd14>3.0.co;2-d.

Abstract

Fetuses with degenerative neurological disorders or metabolic diseases rarely exhibit sonographic abnormalities. As a result, prenatal diagnosis, when available, requires invasive testing. Prenatal diagnosis of spinal muscular atrophy (SMA) can be made by testing chorionic villi or amniocytes. Indirect genotype analysis by use of single- and multi-locus polymorphic microsatellites of the region 5q11.2-q13.3 is used. We present two cases of SMA that manifested at 11 and 16 weeks' gestation by the presence of abnormal ultrasound findings. Each case also had abnormal maternal serum screening.

Publication types

  • Case Reports

MeSH terms

  • Chorionic Gonadotropin / blood*
  • Chorionic Villi Sampling
  • DNA / analysis
  • Estriol / blood*
  • Female
  • Humans
  • Muscular Atrophy, Spinal / blood*
  • Muscular Atrophy, Spinal / diagnostic imaging*
  • Muscular Atrophy, Spinal / genetics
  • Polymerase Chain Reaction
  • Pregnancy
  • Ultrasonography, Prenatal*
  • alpha-Fetoproteins / analysis*

Substances

  • Chorionic Gonadotropin
  • alpha-Fetoproteins
  • DNA
  • Estriol