Non-infective colitis in infancy: evidence in favour of minor immunodeficiency in its pathogenesis

Arch Dis Child. 1997 Apr;76(4):345-8. doi: 10.1136/adc.76.4.345.

Abstract

Forty two infants below the age of 2 years presenting with chronic non-infective diarrhoea and shown to have histologically proved colitis were investigated over a five year period. Allergic colitis was the most common cause of colitis, accounting for 62% of the cases. Other colitides diagnosed included: non-specific colitis, autoimmune enterocolitis, and ulcerative colitis accounting for 10% each; severe combined immunodeficiency 7%, and Crohn's disease 3%. A positive family history and a personal history of atopy were obtained in 48% and 29% of the cases respectively. Serum immunoglobulin A, IgG2, and IgG4 were very low in over 50% of the entire cohort of infants with colitis; 66% of those with severe combined immunodeficiency, autoimmune enterocolitis, and ulcerative colitis (n = 11) had low CD3 and CD4 T lymphocytes with an accompanying increase in CD8 in two thirds of those with severe combined immunodeficiency. T lymphocytes were normal in those with allergic colitis. Thus infants with proved non-infective colitis as a group show a high prevalence of IgA, IgG2, and IgG4 deficiency. It is likely that this minor deficiency of mucosa associated immunoglobulin production has a role in the pathogenesis of the colitic process.

MeSH terms

  • Autoimmune Diseases / immunology
  • CD3 Complex / analysis
  • CD4-CD8 Ratio
  • Chronic Disease
  • Colitis / immunology*
  • Colitis, Ulcerative / immunology
  • Crohn Disease / immunology
  • Diarrhea / immunology*
  • Dysgammaglobulinemia / complications*
  • Dysgammaglobulinemia / immunology
  • Enterocolitis / immunology
  • Humans
  • Hypersensitivity / complications*
  • Hypersensitivity / immunology
  • IgA Deficiency / complications
  • IgA Deficiency / immunology
  • IgG Deficiency / complications
  • IgG Deficiency / immunology
  • Immunity, Mucosal
  • Infant
  • Severe Combined Immunodeficiency / immunology
  • T-Lymphocytes / immunology

Substances

  • CD3 Complex