Human/mouse radiation chimera generated from PBMC of B chronic lymphocytic leukemia patients with autoimmune hemolytic anemia produce anti-human red cell antibodies

Leukemia. 1997 May;11(5):687-93. doi: 10.1038/sj.leu.2400645.

Abstract

Previous studies performed in our laboratory have shown that B-CLL cells are involved in the production of anti-red cell auto-antibodies, providing a possible mechanism for the autoimmune hemolytic anemia occurring during the course of B-CLL. In order to confirm this hypothesis, we attempted to transfer human B-CLL with AIHA to immunodeficient mice. Peripheral blood mononuclear cells (PBMC) from 11 B-CLL patients suffering from AIHA were transplanted into the peritoneal cavity of lethally irradiated Balb/c mice reconstituted with SCID bone marrow. Chimeric mice generated from PBMC of these patients (in stage III-IV of the disease) exhibited an engraftment profile with dominance of tumor cells and minuscule levels of T cells. Eighty-five percent of the chimeric mice generated from 10 out of the 11 B-CLL patients with Coombs'-positive AIHA, produced human Ig with anti-human red cell specificity as detected by indirect anti-globulin test. In addition, anti-red cell auto-antibodies were produced in 36% of chimeric mice generated from PBMC of Coombs'-negative B-CLL. In contrast, control experiments in which splenic cells from idiopathic AIHA or PBMC from normal donors were transplanted, failed to produce anti-RBC. This in vivo model further supports the relationship between the B cell expansion and the autoimmune hemolytic process.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Aged, 80 and over
  • Anemia, Hemolytic / blood
  • Anemia, Hemolytic / complications*
  • Anemia, Hemolytic / immunology
  • Anemia, Hemolytic / pathology
  • Animals
  • Antibody Formation
  • B-Lymphocytes / immunology*
  • Bone Marrow Cells
  • Burkitt Lymphoma / blood
  • Burkitt Lymphoma / complications
  • Burkitt Lymphoma / immunology*
  • Burkitt Lymphoma / pathology
  • Humans
  • Immunophenotyping
  • Lymphocyte Depletion
  • Lymphocyte Transfusion*
  • Mice
  • Mice, Inbred BALB C
  • Mice, Inbred NOD
  • Mice, SCID
  • Middle Aged
  • Neoplasm Staging
  • Radiation Chimera*
  • Reference Values
  • Spleen / immunology
  • T-Lymphocytes / immunology
  • Transplantation, Heterologous