The amino-terminal region of Tyk2 sustains the level of interferon alpha receptor 1, a component of the interferon alpha/beta receptor

Proc Natl Acad Sci U S A. 1997 Oct 28;94(22):11839-44. doi: 10.1073/pnas.94.22.11839.

Abstract

Tyk2 belongs to the Janus kinase (JAK) family of receptor associated tyrosine kinases, characterized by a large N-terminal region, a kinase-like domain and a tyrosine kinase domain. It was previously shown that Tyk2 contributes to interferon-alpha (IFN-alpha) signaling not only catalytically, but also as an essential intracellular component of the receptor complex, being required for high affinity binding of IFN-alpha. For this function the tyrosine kinase domain was found to be dispensable. Here, it is shown that mutant cells lacking Tyk2 have significantly reduced IFN-alpha receptor 1 (IFNAR1) protein level, whereas the mRNA level is unaltered. Expression of the N-terminal region of Tyk2 in these cells reconstituted wild-type IFNAR1 level, but did not restore the binding activity of the receptor. Studies of mutant Tyk2 forms deleted at the N terminus indicated that the integrity of the N-terminal region is required to sustain IFNAR1. These studies also showed that the N-terminal region does not directly modulate the basal autophosphorylation activity of Tyk2, but it is required for efficient in vitro IFNAR1 phosphorylation and for rendering the enzyme activatable by IFN-alpha. Overall, these results indicate that distinct Tyk2 domains provide different functions to the receptor complex: the N-terminal region sustains IFNAR1 level, whereas the kinase-like domain provides a function toward high affinity ligand binding.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Cell Line
  • Enzyme Activation
  • Interferon-alpha / metabolism*
  • Membrane Proteins
  • Mutation
  • Phosphorylation
  • Protein-Tyrosine Kinases*
  • Proteins / genetics
  • Proteins / metabolism*
  • RNA, Messenger / analysis
  • Receptor, Interferon alpha-beta
  • Receptors, Interferon / biosynthesis*
  • Sequence Deletion
  • Signal Transduction
  • Structure-Activity Relationship

Substances

  • Interferon-alpha
  • Membrane Proteins
  • Proteins
  • RNA, Messenger
  • Receptors, Interferon
  • Receptor, Interferon alpha-beta
  • Protein-Tyrosine Kinases